PPIDT00182

Drug Information
NameCaplacizumab
SequenceEVQLVESGGGLVQPGGSLRLSCAASGRTFSYNPMGWFRQAPGKGRELVAAISRTGGSTYYPDSVEGRFTISRDNAKRMVYLQMNSLRAEDTAVYYCAAAGVRAEDGRVRTLPSEYTFWGQGTQVTVSSAAAEVQLVESGGGLVQPGGSLRLSCAASGRTFSYNPMGWFRQAPGKGRELVAAISRTGGSTYYPDSVEGRFTISRDNAKRMVYLQMNSLRAEDTAVYYCAAAGVRAEDGRVRTLPSEYTFWGQGTQVTVSS
DrugBank_IDDB06081
Typebiotech
IndicationCapacizumab is approved for the treatment of adults experiencing an episode of acquired thrombotic thrombocytopenic purpura (aTTP) in conjunction with plasma exchange and immunosuppression in patients 18 years or older.[A174634, L5302] aTTP is a rare autoimmune condition presented by a disruption of blood clotting order which is translated into systemic microvascular thrombosis leading to profound thrombocytopenia, hemolytic anemia and organ ischemia. It is caused by the production of autoantibodies against ADAMTS-13 which is the protein in charge of cleaving the von-Wilebrand factor. The lack of this process produces the generation of ultra large von Wilebrand multimers that bind to platelets and form microthrombi and causing thromboembolic complications.[A174649] Previously, capacizumab was under review for the prevention of thrombosis in high-risk patients with acute coronary syndrome undergoing percutaneous coronary intervention but this indication was withdrawn.[A174634]

Dosage Forms
Form Route Strength
Injection, powder, for solution Intravenous; Subcutaneous
10 mg
Injection, powder, for solution Parenteral; Subcutaneous
10 MG
Injection, powder, lyophilized, for solution; kit Intravenous; Subcutaneous
11 mg/1mL
Kit; powder, for solution Intravenous; Subcutaneous
11 mg / vial
Injection, powder, for solution Parenteral
10 mg/1ml
Injection, powder, lyophilized, for solution Intravenous; Subcutaneous
10 mg
Injection, powder, lyophilized, for solution Intravenous; Subcutaneous
1000000 mg
Target Information
Role Uniprot_ID Gene_Name Entity_Name Organism Actions Internal link
target P04275 VWF von Willebrand factor Homo sapiens inhibitor Link